Amyloid light-chain deposition in a schwannoma
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چکیده
منابع مشابه
Light chain deposition disease presenting with hepatomegaly: an association with amyloid-like fibrils.
We report an unusual case of lambda light chain deposits without overt plasma cell dyscrasia. The clinical presentation was hepatomegaly without biochemical sign of renal involvement. Portal hypertension, spontaneous rupture of the spleen and fracture of the 12th thoracic vertebra occurred during the course of the disease. Ultrastructural studies showed that lambda light chain deposits were ass...
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ژورنال
عنوان ژورنال: Interdisciplinary Neurosurgery
سال: 2021
ISSN: 2214-7519
DOI: 10.1016/j.inat.2021.101301